| | ORTHOLOGY: K08764 | |
Entry |
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Symbol |
SCP2, SCPX
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Name |
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Pathway |
map01040 | Biosynthesis of unsaturated fatty acids |
|
Module |
M00104 | Bile acid biosynthesis, cholesterol => cholate/chenodeoxycholate |
M00861 | beta-Oxidation, peroxisome, VLCFA |
M00862 | beta-Oxidation, peroxisome, tri/dihydroxycholestanoyl-CoA => choloyl/chenodeoxycholoyl-CoA |
|
Reaction |
R03719 | 3alpha,7alpha,12alpha-trihydroxy-5beta-cholanoyl-CoA:propanoyl-CoA C-acyltransferase |
R04811 | propanoyl-CoA:acetyl-CoA C-acyltransferase |
R07937 | (4Z,7Z,10Z,13Z,16Z,19Z)-docosahexaenoyl-CoA:acetyl-CoA C-acyltransferase |
R07953 | (4Z,7Z,10Z,13Z,16Z)-docosapentaenoyl-CoA:acetyl-CoA C-acyltransferase |
|
Disease |
H00407 | Peroxisomal beta-oxidation enzyme deficiency |
H00874 | Leukoencephalopathy with dystonia and motor neuropathy |
|
Brite |
KEGG Orthology (KO) [BR:ko00001]
09100 Metabolism
09103 Lipid metabolism
00120 Primary bile acid biosynthesis
K08764 SCP2, SCPX; sterol carrier protein 2
01040 Biosynthesis of unsaturated fatty acids
K08764 SCP2, SCPX; sterol carrier protein 2
09140 Cellular Processes
09141 Transport and catabolism
04146 Peroxisome
K08764 SCP2, SCPX; sterol carrier protein 2
09150 Organismal Systems
09152 Endocrine system
03320 PPAR signaling pathway
K08764 SCP2, SCPX; sterol carrier protein 2
Enzymes [BR:ko01000]
2. Transferases
2.3 Acyltransferases
2.3.1 Transferring groups other than aminoacyl groups
2.3.1.176 propanoyl-CoA C-acyltransferase
K08764 SCP2, SCPX; sterol carrier protein 2
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Other DBs |
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Genes |
» show all
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Reference |
|
Authors |
Russell DW |
Title |
The enzymes, regulation, and genetics of bile acid synthesis. |
Journal |
|
Reference |
|
Authors |
Stanley WA, Filipp FV, Kursula P, Schuller N, Erdmann R, Schliebs W, Sattler M, Wilmanns M |
Title |
Recognition of a functional peroxisome type 1 target by the dynamic import receptor pex5p. |
Journal |
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Sequence |
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Reference |
|
Authors |
Ferdinandusse S, Denis S, Mooijer PA, Zhang Z, Reddy JK, Spector AA, Wanders RJ |
Title |
Identification of the peroxisomal beta-oxidation enzymes involved in the biosynthesis of docosahexaenoic acid. |
Journal |
J Lipid Res 42:1987-95 (2001) |
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