Entry |
|
Symbol |
ECHS1
|
Name |
|
Pathway |
map00280 | Valine, leucine and isoleucine degradation |
map01110 | Biosynthesis of secondary metabolites |
map01120 | Microbial metabolism in diverse environments |
|
Module |
M00013 | Malonate semialdehyde pathway, propanoyl-CoA => acetyl-CoA |
M00032 | Lysine degradation, lysine => saccharopine => acetoacetyl-CoA |
M00085 | Fatty acid elongation in mitochondria |
|
Reaction |
R02685 | (3S)-3-hydroxyacyl-CoA hydro-lyase |
R03026 | (S)-3-hydroxybutanoyl-CoA hydro-lyase |
R03045 | 3-hydroxypropionyl-CoA hydro-lyase |
R04137 | 3-hydroxyisovaleryl-CoA hydro-lyase |
R04170 | (S)-3-hydroxydodecanoyl-CoA hydro-lyase |
R04204 | (2S,3S)-3-hydroxy-2-methylbutanoyl-CoA hydro-liase |
R04224 | (S)-3-hydroxyisobutyryl-CoA hydro-lyase |
R04738 | (S)-3-hydroxyhexadecanoyl-CoA hydro-lyase |
R04740 | (S)-3-hydroxytetradecanoyl-CoA hydro-lyase |
R04744 | (S)-hydroxydecanoyl-CoA hydro-lyase |
R04746 | (S)-hydroxyoctanoyl-CoA hydro-lyase |
R04749 | (S)-hydroxyhexanoyl-CoA hydro-lyase |
R06942 | (3S)-3-hydroxyacyl-CoA hydro-lyase |
|
Disease |
H00525 | Disorders of mitochondrial fatty-acid oxidation |
|
Brite |
KEGG Orthology (KO) [BR:ko00001]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
K07511 ECHS1; enoyl-CoA hydratase
00650 Butanoate metabolism
K07511 ECHS1; enoyl-CoA hydratase
09103 Lipid metabolism
00062 Fatty acid elongation
K07511 ECHS1; enoyl-CoA hydratase
00071 Fatty acid degradation
K07511 ECHS1; enoyl-CoA hydratase
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
K07511 ECHS1; enoyl-CoA hydratase
00310 Lysine degradation
K07511 ECHS1; enoyl-CoA hydratase
00380 Tryptophan metabolism
K07511 ECHS1; enoyl-CoA hydratase
09106 Metabolism of other amino acids
00410 beta-Alanine metabolism
K07511 ECHS1; enoyl-CoA hydratase
09111 Xenobiotics biodegradation and metabolism
00627 Aminobenzoate degradation
K07511 ECHS1; enoyl-CoA hydratase
00930 Caprolactam degradation
K07511 ECHS1; enoyl-CoA hydratase
Enzymes [BR:ko01000]
4. Lyases
4.2 Carbon-oxygen lyases
4.2.1 Hydro-lyases
4.2.1.17 enoyl-CoA hydratase
K07511 ECHS1; enoyl-CoA hydratase
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Other DBs |
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Genes |
» show all
|
Reference |
|
Authors |
Janssen U, Davis EM, Le Beau MM, Stoffel W |
Title |
Human mitochondrial enoyl-CoA hydratase gene (ECHS1): structural organization and assignment to chromosome 10q26.2-q26.3. |
Journal |
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Sequence |
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