Entry |
|
Name |
Imiglucerase (USAN/INN); Imiglucerase (genetical recombination) (JAN); Cerezyme (TN) |
Product |
|
Formula |
C2532H3843N671O711S16
|
Exact mass |
55537.0717
|
Mol weight |
55571.74
|
Sequence |
ARPCIPKSFG YSSVVCVCNA TYCDSFDPPT FPALGTFSRY ESTRSGRRME LSMGPIQANH TGTGLLLTLQ PEQKFQKVKG FGGAMTDAAA LNILALSPPA QNLLLKSYFS EEGIGYNIIR VPMASCDFSI RTYTYADTPD DFQLHNFSLP EEDTKLKIPL IHRALQLAQR PVSLLASPWT SPTWLKTNGA VNGKGSLKGQ PGDIYHQTWA RYFVKFLDAY AEHKLQFWAV TAENEPSAGL LSGYPFQCLG FTPEHQRDFI ARDLGPTLAN STHHNVRLLM LDDQRLLLPH WAKVVLTDPE AAKYVHGIAV HWYLDFLAPA KATLGETHRL FPNTMLFASE ACVGSKFWEQ SVRLGSWDRG MQYSHSIITN LLYHVVGWTD WNLALNPEGG PNWVRNFVDS PIIVDITKDT FYKQPMFYHL GHFSKFIPEG SQRVGLVASQ KNDLDAVALM HPDGSAVVVV LNRSSKDVPL TIKDPAVGFL ETISPGYSIH TYLWHRQ |
Type |
Peptide |
Remark |
Therapeutic category: | 3959 |
|
Efficacy |
Lysosomal storage disease treatment, Enzyme replacement (glucocerebrosidase) |
Disease |
|
Type |
Enzyme replacement therapy product |
Target |
|
Pathway |
|
Network |
|
Brite |
Anatomical Therapeutic Chemical (ATC) classification [BR:br08303]
A ALIMENTARY TRACT AND METABOLISM
A16 OTHER ALIMENTARY TRACT AND METABOLISM PRODUCTS
A16A OTHER ALIMENTARY TRACT AND METABOLISM PRODUCTS
A16AB Enzymes
A16AB02 Imiglucerase
D03020 Imiglucerase (USAN/INN) <JP/US>
USP drug classification [BR:br08302]
Genetic, Enzyme, or Protein Disorder: Replacement, Modifiers, Treatment
Imiglucerase
D03020 Imiglucerase (USAN/INN)
Therapeutic category of drugs in Japan [BR:br08301]
3 Agents affecting metabolism
39 Other agents affecting metabolism
395 Enzyme preparations
3959 Others
D03020 Imiglucerase (USAN/INN); Imiglucerase (genetical recombination) (JAN)
Target-based classification of drugs [BR:br08310]
Enzymes
Hydrolases (EC3)
Glycosidases
GBA* [HSA_VAR:2629v1]
D03020 Imiglucerase (USAN/INN) <JP/US>
New drug approvals in Europe [br08329.html]
European public assessment reports (EPAR) authorised medicine
D03020
Pharmacogenomic biomarkers [br08341.html]
Germline mutations in genetic disorder treatments
D03020
|
Other DBs |
|